Clinical outcomes in Caroli disease and Caroli syndrome: a longitudinal observational cohort study
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Researchers have been studying Caroli disease and Caroli syndrome, with some focusing on clinical outcomes and others exploring specific presentations, such as portal hypertension or chronic abdominal pain. The conditions appear to be associated with various complications, including extrahepatic biliary obstruction, scoliosis, and recurrent fever. The studies suggest that Caroli disease and syndrome can manifest in different ways, with some cases involving rare or unusual symptoms and radiological findings.
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